A Rare Case of Evan Syndrome with Portal Hypertension
DOI:
https://doi.org/10.12974/2312-5411.2014.01.02.1Keywords:
Evans, Autoimmune, Thrombocytopenia.Abstract
Evan’s syndrome was first described in 1951 by Evan’s and associates. It has long been considered as a coincidental combination of ITP and AIHA and or immune neutropenia in the absence of any underlying cause. We report this rare condition in a 9-year-old male who presented with severe pallor and multiple ecchymotic patches over arms and abdomen with portal hypertension.
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